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Successful pregnancy in a severely hypoxemic patient with pulmonary alveolar proteinosis
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Orientador(es)
Resumo(s)
Abstract
Pulmonary alveolar proteinosis (PAP) is a rare disorder characterized by abnormal accumulation
of a lipoproteinaceous material in the alveoli, which may lead to respiratory failure and has an
associated high risk for infections. The mainstay treatment for PAP is whole lung lavage.
A pregnant woman, previously diagnosed with primary PAP, the most common form of PAP, was
admitted with dyspnea and worsening respiratory function. In one month period, a wholelung
bronchopulmonary lavage was performed twice, with clinical and functional improvement.
Pregnancy was carried to term and a healthy baby was delivered.
The mechanisms of respiratory impairment are discussed as well as treatment options and
response. Resumo
A proteinose alveolar pulmonar (PAP) é uma doença rara caracterizada pela acumulação anormal
de material lipoproteináceo nos alvéolos, que pode levar a insufi ciência respiratória, estando
associada a um risco elevado de infecções. O tratamento gold-standard da PAP é a lavagem
pulmonar total.
Descrição
Palavras-chave
Pregnancy Pulmonary alveolar proteinosis Pulmonary lavage Respiratory failure Gravidez Proteinose alveolar Pulmonar Lavagem pulmonar Insuficiência respiratória
Contexto Educativo
Citação
Rev Port Pneumol. 2011 May-Jun;17(3):139-42
Editora
Revista portuguesa de pneumologia