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Publicação
Chronic granulomatous disease as a risk factor for cutaneous lupus in childhood
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Orientador(es)
Resumo(s)
Chronic granulomatous disease (CGD) is a primaryimmunodeficiency disorder that affects the phagocyticcells of the innate immune system. It is characterizedby recurrent or persistent infections with granulomaformation. Lupus-like lesions have been reported incarriers of CGD and less frequently, in patients withCGD. Immunological study in these patients areusually negative. We describe the case of an 8-yearoldboy with CGD who developed chronic and acutecutaneous lupus erythematous with angular cheilitis,oral ulcers, Raynaud phenomenon, and positiveserologies for antinuclear, anticentromere, and anti-Saccharomyces cerevisiae antibodies.
Descrição
Palavras-chave
primary immunodeficiency chronic granulomatous disease lupus erythematous
Contexto Educativo
Citação
Dermatol Online J. 2017 Mar 15;23(3)
Editora
University of California, Davis